Chronic thromboembolic pulmonary hypertension in Behçet's disease: effectiveness of endarterectomy

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Department of Autoimmune Diseases, Hospital Clínic-Institut d'Investigacions Biomèdiques Pi i Sunyer (IDIBAPS), Universitat de Barcelona, Spain. gespino@clinic.ub.es

CER858 Submission on line
2010 Vol.28, N°4 ,Suppl.60 - PI 0079, PF 0081
Case Report

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Rheumatology Article



Behçet`s disease is a systemic vasculitis characterised by recurrent mouth and genital ulcers and uveitis. About 25% of patients suffer from vascular involvement. We describe a patient with Behçet`s disease who suffered recurrent pulmonary embolism and developed severe chronic thromboembolic pulmonary hypertension. The patient was successfully treated with pulmonary endarterectomy that normalised pulmonary haemodynamics. Chronic thromboembolic pulmonary hypertension is a potential complication of Behçet`s disease that may be amenable to pulmonary endarterectomy.

PMID: 20868576 [PubMed]

Received: 27/01/2010 - Accepted : 23/04/2010 - In Press: 24/09/2010 - Published: 24/09/2010