Case Reports
Coronary aneurysms in a child: an unusual presentation of pseudovasculitis
L.P. Seguro, J. Freire De Carvalho, A.C. Lianza, R.M. Pereira
CER5347
2013 Vol.31, N°1
PI 0125, PF 0127
Case Reports
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PMID: 23137568 [PubMed]
Received: 30/12/2011
Accepted : 16/05/2012
In Press: 08/11/2012
Published: 28/01/2013
Abstract
Abnormalities of the coronary arteries in children are rare and Kawasaki disease is the most common cause of acquired coronary disease in a paediatric population. We report a case of a female child with coronary artery aneurysms and convulsions, who was diagnosed with Kawasaki disease. Due to systemic arterial hypertension and persistence of high inflammatory markers after treatment with high dose glucocorticoid and intravenous immunoglobulin, further investigation was performed and revealed a pheochromocytoma. Surgical removal led to normalization of blood pressure and laboratory parameters. Periodic echocardiography studies revealed progressive reduction of coronary aneurysms, with complete normalisation after 8 months. This is the first case described of coronary aneurysms presenting as a pseudovasculitis syndrome associated with pheochromocytoma.