Case Reports
Juvenile eosinophilic fasciitis: three case reports with review of the literature.
R. Papa1, P. Nozza2, C. Granata3, R. Caorsi4, M. Gattorno5, A. Martini6, P. Picco7
- UOC Pediatria II, Reumatologia, Istituto Giannina Gaslini, Genoa, Italy. papariccardo86@gmail.com
- UOC Anatomia patologica, Istituto Giannina Gaslini, Genoa, Italy.
- UOC Radiologia, Istituto Giannina Gaslini, Genoa, Italy.
- UOC Pediatria II, Reumatologia, Istituto Giannina Gaslini, Genoa, Italy.
- UOC Pediatria II, Reumatologia, Istituto Giannina Gaslini, Genoa, Italy.
- Università degli Studi di Genova, Genoa, Italy.
- UOC Pediatria II, Reumatologia, Istituto Giannina Gaslini, Genoa, Italy.
CER8687
2016 Vol.34, N°3
PI 0527, PF 0530
Case Reports
Free to view
(click on article PDF icon to read the article)
PMID: 27268780 [PubMed]
Received: 13/06/2015
Accepted : 26/10/2015
In Press: 30/05/2016
Published: 30/05/2016
Abstract
OBJECTIVES:
Eosinophilic fasciitis is an uncommon scleroderma-like disorder characterised by induration and thickening of skin and soft tissue, usually associated with peripheral eosinophilia, poorly characterised in childhood.
METHODS:
We report 3 paediatric cases of eosinophilic fasciitis showing unusual clinical and histopathological features with a review of the literature.
RESULTS:
All cases presented progressive motility impairment started from upper limbs with no skin abnormalities. All cases showed systemic inflammatory involvement and 2 patients had acute complications. Two patients developed disabling outcomes despite appropriate treatments.
CONCLUSIONS:
Eosinophilic fasciitis may present unusual clinical and histopathological features during childhood and requires early recognition in order to prevent acute complications and disabling outcomes.
