2025 Vol.43, N°10 - Table of contents
October - Behçet's Disease and other Autoinflammatory Conditions - n. 25
One year in review
CER19240
2025,43,10
Pg. 1699-1708
Free to view
Behçet's syndrome: one year in review 2025
G. Hatemi, E. Seyahi, I. Fresko, R. Talarico, D. Uçar, V. Hamuryudan
DOI: https://doi.org/10.55563/clinexprheumatol/8xuim0
G. Hatemi, E. Seyahi, I. Fresko, R. Talarico, D. Uçar, V. Hamuryudan
DOI: https://doi.org/10.55563/clinexprheumatol/8xuim0
Environmental Rheumatology
CER18421
2025,43,10
Pg. 1709-1714
Free to view
Prevalence, incidence and geographic distribution of familial Mediterranean fever in Turkey: a national cohort study
H. Satiş, A. Gül, G. Ayan, H. Babaoğlu, B. Armağan, A. Erden, E. Bilgin, E. Karabulut, L. Kiliç, D. Tecer, A. Sari, O. Küçükşahin, S. Uğurlu, Ö. Kasapçopur, S. Özen, M.O. Ayvali, A.A. Fidanci, M.M. Ülgü, N. Ata, Ş. Birinci, U. Kalyoncu
DOI: https://doi.org/10.55563/clinexprheumatol/pzbg88
H. Satiş, A. Gül, G. Ayan, H. Babaoğlu, B. Armağan, A. Erden, E. Bilgin, E. Karabulut, L. Kiliç, D. Tecer, A. Sari, O. Küçükşahin, S. Uğurlu, Ö. Kasapçopur, S. Özen, M.O. Ayvali, A.A. Fidanci, M.M. Ülgü, N. Ata, Ş. Birinci, U. Kalyoncu
DOI: https://doi.org/10.55563/clinexprheumatol/pzbg88
Editorial
CER19172
2025,43,10
Pg. 1715-1717
Free to view
The decline of AA amyloidosis in familial Mediterranean fever is significant, but the story is not over
A. Gül, E. Ben-Chetrit
DOI: https://doi.org/10.55563/clinexprheumatol/qdl1yj
A. Gül, E. Ben-Chetrit
DOI: https://doi.org/10.55563/clinexprheumatol/qdl1yj
Full Papers
CER18061
2025,43,10
Pg. 1718-1725
Free to view
Distinct features of trisomy 8-associated autoinflammatory disease from Behçet's disease: case series and systematic review
K. Ichikawa, S. Adachi, K. Takase-Minegishi, Y. Nakayama, Y. Nagasawa, Y. Iizuka, A. Maeda, L. Hirahara, Y. Soejima, T. Ohashi, H. Kunimoto, N. Horita, R. Yoshimi, Y. Kirino, H. Nakajima
DOI: https://doi.org/10.55563/clinexprheumatol/8j7rbr
K. Ichikawa, S. Adachi, K. Takase-Minegishi, Y. Nakayama, Y. Nagasawa, Y. Iizuka, A. Maeda, L. Hirahara, Y. Soejima, T. Ohashi, H. Kunimoto, N. Horita, R. Yoshimi, Y. Kirino, H. Nakajima
DOI: https://doi.org/10.55563/clinexprheumatol/8j7rbr
CER18064
2025,43,10
Pg. 1726-1734
Free to view
Clinicopathological characteristics of severe aortic valve regurgitation caused by Behçet’s syndrome
M. Zhang, X. Wang, Y. Liu, X. Liu, X. Yu, L. Sun, Z. Wang, L. Zhang, J. Liu, G. Ma, W. Chen, W. Wang, Q. Miao, W. Zheng
DOI: https://doi.org/10.55563/clinexprheumatol/k2v1he
M. Zhang, X. Wang, Y. Liu, X. Liu, X. Yu, L. Sun, Z. Wang, L. Zhang, J. Liu, G. Ma, W. Chen, W. Wang, Q. Miao, W. Zheng
DOI: https://doi.org/10.55563/clinexprheumatol/k2v1he
CER18235
2025,43,10
Pg. 1735-1741
Free to view
A single dose of anakinra for arresting familial Mediterranean fever attacks: a proof-of-concept study
E. Giat, A. Livneh, I. Ben-Zvi, A. Druyan, D. Bar, D.J. Ozeri, G. Almoznino, M. Lidar
DOI: https://doi.org/10.55563/clinexprheumatol/cj61ub
E. Giat, A. Livneh, I. Ben-Zvi, A. Druyan, D. Bar, D.J. Ozeri, G. Almoznino, M. Lidar
DOI: https://doi.org/10.55563/clinexprheumatol/cj61ub
CER18454
2025,43,10
Pg. 1742-1747
Free to view
Can nailfold capillaroscopy findings be a marker for uveitis in Behçet's syndrome?
S. Zontul, E. Inanç, A. Can, Ş.T. Tay, H. Çolak, T. Cumurcu, S. Yolbas
DOI: https://doi.org/10.55563/clinexprheumatol/iunbq7
S. Zontul, E. Inanç, A. Can, Ş.T. Tay, H. Çolak, T. Cumurcu, S. Yolbas
DOI: https://doi.org/10.55563/clinexprheumatol/iunbq7
CER18531
2025,43,10
Pg. 1748-1752
Free to view
A novel AGBL3 variant potentially associated with hypocomplementaemic urticarial vasculitis syndrome: examining clinical outcomes and therapeutic responses
B. Karacam, I. Khan, A. Hacisuleyman, C. Bracaglia, N. Abaci, S. Sirma-Ekmekci, A. Gül
DOI: https://doi.org/10.55563/clinexprheumatol/85pdxt
B. Karacam, I. Khan, A. Hacisuleyman, C. Bracaglia, N. Abaci, S. Sirma-Ekmekci, A. Gül
DOI: https://doi.org/10.55563/clinexprheumatol/85pdxt
CER18663
2025,43,10
Pg. 1753-1762
Free to view
IL-1 targeting agents in Schnitzler syndrome: a multicentre, real-world study from the international AIDA Network Schnitzler Registry
L. Calabrese, A. Cartocci, A. Vitale, E. Martín-Nares, M. D’onghia, V. Caggiano, J. Torres-Ruiz, R. Lopez, K. Jahnz-Rozyk, K. Rybak, M. Frassi, F. Franceschini, F. Crisafulli, A. Tufan, H. Kucuk, A. Avanoglu Guler, A. Gidaro, L. La Cava, F. Della Casa, I. Mormile, E. Cinotti, G. Lopalco, J. Sota, J. Sbalchiero, G. Emmi, A. Recke, S. Costi, P. Sfriso, S. Monti, O. Viapiana, A. Hinojosa-Azaola, A. Balistreri, C. Fabiani, B. Frediani, P. Rubegni, E. Wiesik-Szewczyk, L. Cantarini
DOI: https://doi.org/10.55563/clinexprheumatol/i9hsfr
L. Calabrese, A. Cartocci, A. Vitale, E. Martín-Nares, M. D’onghia, V. Caggiano, J. Torres-Ruiz, R. Lopez, K. Jahnz-Rozyk, K. Rybak, M. Frassi, F. Franceschini, F. Crisafulli, A. Tufan, H. Kucuk, A. Avanoglu Guler, A. Gidaro, L. La Cava, F. Della Casa, I. Mormile, E. Cinotti, G. Lopalco, J. Sota, J. Sbalchiero, G. Emmi, A. Recke, S. Costi, P. Sfriso, S. Monti, O. Viapiana, A. Hinojosa-Azaola, A. Balistreri, C. Fabiani, B. Frediani, P. Rubegni, E. Wiesik-Szewczyk, L. Cantarini
DOI: https://doi.org/10.55563/clinexprheumatol/i9hsfr
CER18763
2025,43,10
Pg. 1763-1771
Free to view
Predictors of post-operative cardiovascular complications for Behçet’s disease with pre-operative immunosuppressive therapy
L. Ye, F. Chen, W. Wang, O. Chen, H. Qing, L. Gan, L. Zhuang, Y. Cui, X. Jian
DOI: https://doi.org/10.55563/clinexprheumatol/gkx830
L. Ye, F. Chen, W. Wang, O. Chen, H. Qing, L. Gan, L. Zhuang, Y. Cui, X. Jian
DOI: https://doi.org/10.55563/clinexprheumatol/gkx830
CER18801
2025,43,10
Pg. 1772-1781
Free to view
The relationship between NETosis findings and disease activity in Behçet's disease: an exploratory study
E. Bektas, R. Deniz, Z. Emrence, S. Sirma Ekmekci, N. Abaci, S. Amikishiyev, Y. Yalcinkaya, B. Artim Esen, M. Inanc, A. Gül
DOI: https://doi.org/10.55563/clinexprheumatol/4thkqz
E. Bektas, R. Deniz, Z. Emrence, S. Sirma Ekmekci, N. Abaci, S. Amikishiyev, Y. Yalcinkaya, B. Artim Esen, M. Inanc, A. Gül
DOI: https://doi.org/10.55563/clinexprheumatol/4thkqz
CER18992
2025,43,10
Pg. 1782-1788
Free to view
Behçet's disease beyond the criteria: insights from a tertiary centre in Turkey
B. Firlatan Yazgan, E.A. Sahin Mavi, G.S. Kart Bayram, B. Bulat, M. Ekici, E. Unaldi, G. Sandal Uzun, G. Ayan, Z. Ozsoy, S.A. Germe, B. Farisogullari, E. Duran, G.K. Yardimci, E.C. Bolek, E. Bilgin, B. Armagan, A. Sari, A. Erden, L. Kilic, B. Kisacik, Y. Maras, I. Dogan, O. Karadag, A. Akdogan, S. Apras Bilgen, S. Kiraz, A.I. Ertenli, U. Kalyoncu
DOI: https://doi.org/10.55563/clinexprheumatol/h8mxc6
B. Firlatan Yazgan, E.A. Sahin Mavi, G.S. Kart Bayram, B. Bulat, M. Ekici, E. Unaldi, G. Sandal Uzun, G. Ayan, Z. Ozsoy, S.A. Germe, B. Farisogullari, E. Duran, G.K. Yardimci, E.C. Bolek, E. Bilgin, B. Armagan, A. Sari, A. Erden, L. Kilic, B. Kisacik, Y. Maras, I. Dogan, O. Karadag, A. Akdogan, S. Apras Bilgen, S. Kiraz, A.I. Ertenli, U. Kalyoncu
DOI: https://doi.org/10.55563/clinexprheumatol/h8mxc6
CER19097
2025,43,10
Pg. 1789-1798
Free to view
Identification of clinical phenotypes in Behçet’s syndrome using latent class analysis: a step toward precision medicine
S. Chadli, M. Maamar, R. Abouqal, W. Ammouri, Z. Tazi Mezalek, H. Harmouche
DOI: https://doi.org/10.55563/clinexprheumatol/3dhh59
S. Chadli, M. Maamar, R. Abouqal, W. Ammouri, Z. Tazi Mezalek, H. Harmouche
DOI: https://doi.org/10.55563/clinexprheumatol/3dhh59
Reviews
CER18043
2025,43,10
Pg. 1799-1809
Free to view
Assessing the efficacy of anticoagulation therapy in the treatment of vascular Behçet's disease: a systematic review
M. Omar, F. Hassan, M.E. Naffaa
DOI: https://doi.org/10.55563/clinexprheumatol/t03f5r
M. Omar, F. Hassan, M.E. Naffaa
DOI: https://doi.org/10.55563/clinexprheumatol/t03f5r
CER18554
2025,43,10
Pg. 1810-1815
Free to view
Promoting patients’ empowerment in rheumatic diseases: the perspective of the International Society of Behçet’s Disease Working Group on Patient Empowerment, Adherence to Therapy and Patients’ Education
F. Di Cianni, D. Marinello, A. Altenburg, U. Karacayli, G. Emmi, M. Schirmer, G. Mumcu, F. Fortune, R. Talarico
on behalf of the International Society of Behçet’s Disease (ISBD) Working Group on Patients Empowerment, Adherence to Therapy and Patients’ Education
DOI: https://doi.org/10.55563/clinexprheumatol/rk42aa
F. Di Cianni, D. Marinello, A. Altenburg, U. Karacayli, G. Emmi, M. Schirmer, G. Mumcu, F. Fortune, R. Talarico
on behalf of the International Society of Behçet’s Disease (ISBD) Working Group on Patients Empowerment, Adherence to Therapy and Patients’ Education
DOI: https://doi.org/10.55563/clinexprheumatol/rk42aa
Paediatric Rheumatology
CER18307
2025,43,10
Pg. 1816-1822
Free to view
On-demand corticosteroid use in the syndrome of undifferentiated recurrent fever: a literature review and results from the JIR-CLiPS survey study
E.D. Batu, S. Sener, M. Rodrigues, C. Vinit, F. Hofer, K. Laskari, R. Craveiro Costa, M. Santos Faria, G. Ozomay Baykal, O. Boyarchuk, O. Gilliaux, K. Pateras, H.E. Sonmez, N. Toplak, M. Gattorno, M. Hofer
DOI: https://doi.org/10.55563/clinexprheumatol/jmtag4
E.D. Batu, S. Sener, M. Rodrigues, C. Vinit, F. Hofer, K. Laskari, R. Craveiro Costa, M. Santos Faria, G. Ozomay Baykal, O. Boyarchuk, O. Gilliaux, K. Pateras, H.E. Sonmez, N. Toplak, M. Gattorno, M. Hofer
DOI: https://doi.org/10.55563/clinexprheumatol/jmtag4
CER18542
2025,43,10
Pg. 1823-1829
Free to view
Clinical predictors of remission in systemic juvenile idiopathic arthritis/Still’s disease: insight from real-life data and the potential relevance of the ‘window of opportunity’
S. Abu-Rumeileh, M.V. Mastrolia, A. Laurent, M. Fouillet-Desjonqueres, F. Zekre, I. Pagnini, E. Marrani, I. Maccora, A. Belot, G. Simonini
DOI: https://doi.org/10.55563/clinexprheumatol/7k95gj
S. Abu-Rumeileh, M.V. Mastrolia, A. Laurent, M. Fouillet-Desjonqueres, F. Zekre, I. Pagnini, E. Marrani, I. Maccora, A. Belot, G. Simonini
DOI: https://doi.org/10.55563/clinexprheumatol/7k95gj
CER18825
2025,43,10
Pg. 1830-1835
Free to view
Silent but significant: subclinical cardiovascular changes in paediatric Behçet’s disease
I. Bingöl, H.E. Sönmez, S. Doğan, H. Bornaun
DOI: https://doi.org/10.55563/clinexprheumatol/hepzdi
I. Bingöl, H.E. Sönmez, S. Doğan, H. Bornaun
DOI: https://doi.org/10.55563/clinexprheumatol/hepzdi
Clinical Vignette
CER19186
2025,43,10
Pg. 1836-1837
Free to view
False aneurysm of the subclavian artery with chest wall destruction
H. Xu, X. Zhang, H. Zhu
DOI: https://doi.org/10.55563/clinexprheumatol/3tstg9
H. Xu, X. Zhang, H. Zhu
DOI: https://doi.org/10.55563/clinexprheumatol/3tstg9
Letters to the Editor
CER18597
2025,43,10
Pg. 1838-1839
Free to view
Inflammatory arthritis as an atypical manifestation of Coffin-Siris syndrome linked to a novel ARID1B variant
S. Matza-Porges, Z. Bar-On, A. Lev, A.J. Simon, H. Peleg, O. Shamriz
DOI: https://doi.org/10.55563/clinexprheumatol/833pi0
S. Matza-Porges, Z. Bar-On, A. Lev, A.J. Simon, H. Peleg, O. Shamriz
DOI: https://doi.org/10.55563/clinexprheumatol/833pi0
CER19098
2025,43,10
Pg. 1840
Free to view
Development of systemic amyloidosis in a patient with heterozygous P369S mutation in the MEFV gene
D. Bulut Gökten, Ö. Atakan Soğur, R. Mercan
DOI: https://doi.org/10.55563/clinexprheumatol/6usbg0
D. Bulut Gökten, Ö. Atakan Soğur, R. Mercan
DOI: https://doi.org/10.55563/clinexprheumatol/6usbg0